4.1.3.4: hydroxymethylglutaryl-CoA lyase
This is an abbreviated version!
For detailed information about hydroxymethylglutaryl-CoA lyase, go to the full flat file.
Word Map on EC 4.1.3.4
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4.1.3.4
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3-hydroxy-3-methylglutaric
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aciduria
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ketogenesis
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hypoglycemia
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acidosis
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inborn
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3-methylglutaric
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3-methylglutaconic
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ketogenic
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3-hydroxyisovaleric
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hyperammonemia
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hypoketotic
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mevalonii
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lethargy
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3-methylcrotonyl-coa
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medicine
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acetoacetyl-coa
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hl-deficient
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hmgcs2
- 4.1.3.4
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3-hydroxy-3-methylglutaric
- aciduria
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ketogenesis
- hypoglycemia
- acidosis
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inborn
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3-methylglutaric
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3-methylglutaconic
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ketogenic
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3-hydroxyisovaleric
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hyperammonemia
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hypoketotic
- mevalonii
- lethargy
- 3-methylcrotonyl-coa
- medicine
- acetoacetyl-coa
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hl-deficient
- hmgcs2
Reaction
Synonyms
3-hydroxy-3-methylglutarate-CoA lyase, 3-Hydroxy-3-methylglutaryl CoA cleaving enzyme, 3-hydroxy-3-methylglutaryl CoA lyase, 3-Hydroxy-3-methylglutaryl coenzyme A lyase, 3-Hydroxy-3-methylglutaryl-CoA lyase, 3-hydroxy-3-methylglutaryl-CoA lyase-like protein, 3-hydroxy-3-methylglutaryl-coenzyme A lyase, 3-hydroxy-methylglutaryl coenzyme A lyase, beta-hydroxy-beta-methylglutaryl-CoA lyase, HCL1, HL, HMG CoA cleavage enzyme, HMG CoA lyase, HMG-CoA lyase, HMGCL, HMGCLL1, HMGL, Hydroxymethylglutaryl coenzyme A lyase, Hydroxymethylglutaryl coenzyme A-cleaving enzyme, LiuE protein
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Natural Substrates Products
Natural Substrates Products on EC 4.1.3.4 - hydroxymethylglutaryl-CoA lyase
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REACTION DIAGRAM
(S)-3-Hydroxy-3-methylglutaryl-CoA
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involved in ketogenesis, leucine catabolism
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(S)-3-Hydroxy-3-methylglutaryl-CoA
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involved in ketogenesis, leucine catabolism
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(S)-3-Hydroxy-3-methylglutaryl-CoA
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involved in regulation of isoprenoid pathway
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(S)-3-Hydroxy-3-methylglutaryl-CoA
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involved in ketogenesis, leucine catabolism
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(S)-3-Hydroxy-3-methylglutaryl-CoA
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acetoacetate as fuel for extrahepatic tissues, involved in mevalonate synthesis
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Acetyl-CoA + acetoacetate
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(S)-3-Hydroxy-3-methylglutaryl-CoA
Acetyl-CoA + acetoacetate
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(S)-3-Hydroxy-3-methylglutaryl-CoA
Acetyl-CoA + acetoacetate
Penicillium brevicompactum ATCC 16024
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(S)-3-Hydroxy-3-methylglutaryl-CoA
Acetyl-CoA + acetoacetate
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