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Literature summary for 4.1.3.4 extracted from

  • Ashmarina, L.I.; Pshezhetsky, A.V.; Branda, S.S.; Isaya, G.; Mitchell, G.A.
    3-Hydroxy-3-methylglutaryl coenzyme A lyase: targeting and processing in peroxisomes and mitochondria (1999), J. Lipid Res., 40, 70-75.
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Homo sapiens 5739
-
peroxisome no activity in lymphoblasts of Zellweger patients Homo sapiens 5777
-

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
31000
-
mitochondrial enzyme, SDS-PAGE Homo sapiens
33000
-
peroxisomal enzyme, SDS-PAGE Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
additional information Homo sapiens last step in ketogenesis ?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
normal and patients with Zellweger syndrome
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
(S)-3-Hydroxy-3-methylglutaryl-CoA
-
Homo sapiens Acetyl-CoA + acetoacetate
-
?
additional information last step in ketogenesis Homo sapiens ?
-
?

Synonyms

Synonyms Comment Organism
HL
-
Homo sapiens