4.1.3.4: hydroxymethylglutaryl-CoA lyase
This is an abbreviated version!
For detailed information about hydroxymethylglutaryl-CoA lyase, go to the full flat file.
Word Map on EC 4.1.3.4
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4.1.3.4
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3-hydroxy-3-methylglutaric
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aciduria
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ketogenesis
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hypoglycemia
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acidosis
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inborn
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3-methylglutaric
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3-methylglutaconic
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ketogenic
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3-hydroxyisovaleric
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hyperammonemia
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hypoketotic
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mevalonii
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lethargy
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3-methylcrotonyl-coa
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medicine
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acetoacetyl-coa
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hl-deficient
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hmgcs2
- 4.1.3.4
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3-hydroxy-3-methylglutaric
- aciduria
-
ketogenesis
- hypoglycemia
- acidosis
-
inborn
-
3-methylglutaric
-
3-methylglutaconic
-
ketogenic
-
3-hydroxyisovaleric
-
hyperammonemia
-
hypoketotic
- mevalonii
- lethargy
- 3-methylcrotonyl-coa
- medicine
- acetoacetyl-coa
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hl-deficient
- hmgcs2
Reaction
Synonyms
3-hydroxy-3-methylglutarate-CoA lyase, 3-Hydroxy-3-methylglutaryl CoA cleaving enzyme, 3-hydroxy-3-methylglutaryl CoA lyase, 3-Hydroxy-3-methylglutaryl coenzyme A lyase, 3-Hydroxy-3-methylglutaryl-CoA lyase, 3-hydroxy-3-methylglutaryl-CoA lyase-like protein, 3-hydroxy-3-methylglutaryl-coenzyme A lyase, 3-hydroxy-methylglutaryl coenzyme A lyase, beta-hydroxy-beta-methylglutaryl-CoA lyase, HCL1, HL, HMG CoA cleavage enzyme, HMG CoA lyase, HMG-CoA lyase, HMGCL, HMGCLL1, HMGL, Hydroxymethylglutaryl coenzyme A lyase, Hydroxymethylglutaryl coenzyme A-cleaving enzyme, LiuE protein
ECTree
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KM Value
KM Value on EC 4.1.3.4 - hydroxymethylglutaryl-CoA lyase
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0.02
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pH 8.2, 30°C, recombinant enzyme
0.024
(S)-3-hydroxy-3-methylglutaryl-CoA
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HMGCLL1 mutant G2A and wild-type HMGCL, pH 8.2, 37°C
0.0134
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K48Q mutant protein, pH not specified in the publication, 30°C
0.0209
3-hydroxy-3-methylglutaryl-CoA
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K48N mutant protein, pH not specified in the publication, 30°C
0.026
3-hydroxy-3-methylglutaryl-CoA
pH not specified in the publication, temperature not specified in the publication
0.0265
3-hydroxy-3-methylglutaryl-CoA
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wild type protein, pH not specified in the publication, 30°C