4.1.1.9: malonyl-CoA decarboxylase
This is an abbreviated version!
For detailed information about malonyl-CoA decarboxylase, go to the full flat file.
Word Map on EC 4.1.1.9
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4.1.1.9
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carnitine
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malonic
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amp-activated
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palmitoyltransferase
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aciduria
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goose
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uropygial
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methylmalonyl-coa
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methylmalonic
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medicine
- 4.1.1.9
- carnitine
-
malonic
-
amp-activated
- palmitoyltransferase
-
aciduria
- goose
-
uropygial
- methylmalonyl-coa
-
methylmalonic
- medicine
Reaction
Synonyms
Acyl-CoA: malonate CoA transferase/malonyl-CoA decarboxylase, Decarboxylase, malonyl coenzyme A, hMCD, malonyl CoA decarboxylase, Malonyl coenzyme A decarboxylase, Malonyl-CoA decarboxylase, malonyl-CoA decarboxylase/acetyltransferase, malonyl-coenzyme A decarboxylase, MCD, MLYCD
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medicine
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enzyme deficiency is associated with mild mental retardation, seizures, hypotonia, cardiomyopathie, vomiting, hypoglycemia, metabolic acidosis and malonic aciduria
medicine
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enzyme deficiency is characterized by malonic aciduria, developmental delay, seizure disorder, and mental retardation
medicine
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MCD is involved in regulating cardiac malonyl-CoA levels, inhibition of MCD can limit rates of fatty acid oxidation, leading to a secondary increase in glucose oxidation associated with an improvement in the functional recovery of the heart during ischaemia/reperfusion injury
medicine
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MCD is involved in regulating cardiac malonyl-CoA levels, inhibition of MCD can limit rates of fatty acid oxidation, leading to a secondary increase in glucose oxidation associated with an improvement in the functional recovery of the heart during ischaemia/reperfusion injury
medicine
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MCD is involved in regulating cardiac malonyl-CoA levels, inhibition of MCD can limit rates of fatty acid oxidation, leading to a secondary increase in glucose oxidation associated with an improvement in the functional recovery of the heart during ischaemia/reperfusion injury