EC Number |
General Information |
Reference |
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1.3.8.7 | malfunction |
medium-chain acyl-CoA dehydrogenase deficiency (OMIM 201450) is the most common inherited disorder of fatty acid metabolism presenting with hypoglycaemia, hepatopathy and Reye-like symptoms during catabolism, genotyping and phenotypes, overview. Functional effects of different medium-chain acyl-CoA dehydrogenase genotypes and identification of asymptomatic variants |
726305 |
1.3.8.7 | metabolism |
acyl-CoA dehydrogenase catalyzes the first reaction step in mitochondrial fatty-acid beta-oxidation |
710755 |
1.3.8.7 | physiological function |
genome sequence reveals 21 putative acyl-CoA dehydrogenases. A mutant with insertionally inactivated isoform PP_1893 grows and accumulates medium chain length polyhydroxyalkanoate on a range of fatty acids as the sole source of carbon and energy |
-, 743247 |
1.3.8.7 | physiological function |
genome sequence reveals 21 putative acyl-CoA dehydrogenases. A mutant with insertionally inactivated isoform PP_2039 grows and accumulates medium chain length polyhydroxyalkanoate on a range of fatty acids as the sole source of carbon and energy |
-, 743247 |
1.3.8.7 | physiological function |
genome sequence reveals 21 putative acyl-CoA dehydrogenases. A mutant with insertionally inactivated isoform PP_2048 grows and accumulates medium chain length polyhydroxyalkanoate on a range of fatty acids as the sole source of carbon and energy |
-, 743247 |
1.3.8.7 | physiological function |
involved in fatty acid oxidation, essential energy generation |
700546 |