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Literature summary extracted from

  • Kumar, M.; Cao, W.; McDaniel, J.K.; Pham, H.P.; Raju, D.; Nawalinski, K.; Frangos, S.; Kung, D.; Zager, E.; Kasner, S.E.; Levine, J.M.; Zheng, X.L.
    Plasma ADAMTS13 activity and von Willebrand factor antigen and activity in patients with subarachnoid haemorrhage (2017), Thromb. Haemost., 117, 691-699 .
    View publication on PubMedView publication on EuropePMC

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
3.4.24.87 von Willebrand factor + H2O Homo sapiens
-
?
-
?

Organism

EC Number Organism UniProt Comment Textmining
3.4.24.87 Homo sapiens Q76LX8
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.4.24.87 blood plasma
-
Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.4.24.87 recombinant human VWF73 peptide + H2O
-
Homo sapiens ?
-
?
3.4.24.87 von Willebrand factor + H2O
-
Homo sapiens ?
-
?

Synonyms

EC Number Synonyms Comment Organism
3.4.24.87 ADAMTS13 a disintegrin and metalloprotease with thrombospondin motifs 13 Homo sapiens
3.4.24.87 von Willebrand cleavage protease
-
Homo sapiens

Expression

EC Number Organism Comment Expression
3.4.24.87 Homo sapiens plasma enzyme activity in aneurysmal subarachnoid haemorrhage patients is significantly lower than that in healthy subjects down

General Information

EC Number General Information Comment Organism
3.4.24.87 malfunction reduced enzyme activity is associated with arterial thrombosis Homo sapiens