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Literature summary extracted from

  • Mihalik, S.J.; Morrell, J.C.; Kim, D.; Sacksteder, K.A.; Watkins, P.A.; Gould, S.J.
    Identification of PAHX, a Refsum disease gene (1997), Nature Genet., 17, 185-189.
    View publication on PubMed

Cloned(Commentary)

EC Number Cloned (Comment) Organism
1.14.11.18 in bacterial expression vector pMALc2 Homo sapiens

Metals/Ions

EC Number Metals/Ions Comment Organism Structure
1.14.11.18 Fe2+ requirement Homo sapiens

Organism

EC Number Organism UniProt Comment Textmining
1.14.11.18 Homo sapiens
-
human
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.14.11.18 phytanoyl-CoA + 2-oxoglutarate + O2
-
Homo sapiens alpha-hydroxyphytanoyl-CoA + succinate + CO2
-
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