Protein Variants | Comment | Organism |
---|---|---|
E220Q | the mutant contains a conserved acidic amino acid mutation that abolishes alpha1,2-mannosidase enzyme activity | Homo sapiens |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
Hep-G2 cell | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
alpha1-antitrypsin null (Hong Kong) + H2O | - |
Homo sapiens | ? + D-mannose | - |
? | |
Glcalpha(1-3)Manalpha(1-2)Manalpha(1-2)Manalpha(1-3)[Manalpha(1-2)Manalpha(1-3)[Manalpha(1-2)Manalpha(1-6)]Manalpha(1-6)]Manbeta(1-4)GlcNAcbeta(1-4)GlcNAc + H2O | - |
Homo sapiens | Glcalpha(1-3)Manalpha(1-2)Manalpha(1-2)Manalpha(1-3)[Manalpha(1-2)Manalpha(1-3)[Manalpha(1-6)]Manalpha(1-6)]Manbeta(1-4)GlcNAcbeta(1-4)GlcNAc + D-mannose | - |
? |
Synonyms | Comment | Organism |
---|---|---|
class I alpha1,2-mannosidase | - |
Homo sapiens |
EDEM1 | - |
Homo sapiens |
ER degradation enhancing alpha-mannosidase-like protein 1 | - |
Homo sapiens |
ER ManI | - |
Homo sapiens |
ER mannosidase I | - |
Homo sapiens |