EC Number   |
BRENDA No. |
Title |
Journal |
Volume |
Pages |
Year |
Organism |
PubMed ID |
|---|
   3.10.1.1 | 757672 |
A phase 1/2 study of intrathecal heparan-N-sulfatase in patients with mucopolysaccharidosis IIIA |
Mol. Genet. Metab. |
118 |
198-205 |
2016 |
Homo sapiens |
27211612 |
| 3.10.1.1 | 757569 |
Glycosaminoglycan levels and structure in a mucopolysaccharidosis IIIA mice and the effect of a highly secreted sulfamidase engineered to cross the blood-brain barrier |
Metab. Brain Dis. |
32 |
203-210 |
2017 |
Homo sapiens |
27585464 |
| 3.10.1.1 | 757675 |
Intrathecal heparan-N-sulfatase in patients with Sanfilippo syndrome type A A phase IIb randomized trial |
Mol. Genet. Metab. |
126 |
121-130 |
2019 |
Homo sapiens |
30528227 |
| 3.10.1.1 | 757698 |
Reduction in brain heparan sulfate with systemic administration of an IgG Trojan horse-sulfamidase fusion protein in the mucopolysaccharidosis type IIIA mouse |
Mol. Pharm. |
15 |
602-608 |
2018 |
Mus musculus |
29251941 |
| 3.10.1.1 | 288763 |
A rapid four column purification of 2-deoxy-D-glucoside-2-sulphamate sulphohydrolase from human liver |
Biochim. Biophys. Acta |
757 |
359-365 |
1983 |
Homo sapiens |
6849981 |
| 3.10.1.1 | 288763 |
A rapid four column purification of 2-deoxy-D-glucoside-2-sulphamate sulphohydrolase from human liver |
Biochim. Biophys. Acta |
757 |
359-365 |
1983 |
Mammalia |
6849981 |
| 3.10.1.1 | 667124 |
An adult Sanfilippo type A patient with homozygous mutation R206P in the sulfamidase gene |
Am. J. Med. Genet. A |
133 |
85-89 |
2005 |
Homo sapiens |
15637719 |
| 3.10.1.1 | 686946 |
Effect of high dose, repeated intra-CSF injection of sulphamidase on neuropathology in MPS IIIA mice |
Genes Brain Behav. |
7 |
740-753 |
2008 |
Homo sapiens |
18518922 |
| 3.10.1.1 | 670475 |
Enzyme-replacement therapy from birth delays the development of behavior and learning problems in mucopolysaccharidosis type IIIA mice |
Pediatr. Res. |
56 |
65-72 |
2004 |
Homo sapiens |
15128919 |
| 3.10.1.1 | 170832 |
Enzymic degradation of heparin. A sulphamidase and a sulphoesterase from Flavobacterium heparinum |
Biochem. J. |
111 |
91-95 |
1969 |
Pedobacter heparinus |
5775690 |
