EC Number   |
Natural Substrates |
|---|
   7.6.2.4 | ATP + H2O + C12-carnitine[side 1] |
- |
| 7.6.2.4 | ATP + H2O + C16-carnitine[side 1] |
- |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
- |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
involved in peroxisomal import of fatty acids and/or fatty acyl-CoAs into the organelle |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
PMp70 is involved in metabolic transport of long chain acyl-CoASs across the peroxisomal membranes |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
enzyme is involved in metabolite transport across the peroxisomal membrane |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
long-chain fatty acids are imported from the cytosolic pool of activated long-chain fatty acids via the peroxisomal membrane proteins Pat1p and Pat2p |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
a defect in the gene for fatty-acyl-CoA-transporting ATPase is responsible for adrenoleukodystrophy, a demyelinating disorder characterized by the accumulation of saturated very-long-chain fatty acids |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
the dysfunction of ALDP is responsible for X-linked adrenoleukodystrophy, a neurodegenerative disorder, loss of ALDP dimerization plays a role in pathogenesis |
| 7.6.2.4 | ATP + H2O + fatty acyl CoA/cis |
enzyme is involved in active transport across the peroxisomal membrane |
