EC Number |
Natural Substrates |
---|
1.5.5.1 | more |
enzyme deficiency leads to glutaric acidemia type II |
1.5.5.1 | more |
genetic regulatory model |
1.5.5.1 | reduced electron-transferring flavoprotein + ubiquinone |
- |
1.5.5.1 | reduced electron-transferring flavoprotein + ubiquinone |
electron transfer via flavin cofactor |
1.5.5.1 | reduced electron-transferring flavoprotein + ubiquinone |
via FAD |
1.5.5.1 | reduced electron-transferring flavoprotein + ubiquinone |
group I electron-transferring flavoprotein, ETF |
1.5.5.1 | reduced electron-transferring-flavoprotein + ubiquinone |
- |
1.5.5.1 | reduced electron-transferring-flavoprotein + ubiquinone |
ETF is the intermediate electron carrier between dehydrogenases and the enzyme, enzyme mediates between eleven mitochondrial proteins and the ubiquinone pool |