EC Number |
Natural Substrates |
---|
1.14.15.4 | 11-deoxy-cortisol + reduced ferredoxin + O2 |
- |
1.14.15.4 | 11-deoxycorticosterone + reduced adrenal ferredoxin + O2 |
11beta-hydroxylation, last 3 steps of pathway for aldosterone biosynthesis |
1.14.15.4 | 11-deoxycorticosterone + reduced adrenodoxin + O2 |
- |
1.14.15.4 | 11-deoxycortisol + adrenal ferredoxin + H2O |
- |
1.14.15.4 | 11-deoxycortisol + reduced adrenal ferredoxin + O2 |
- |
1.14.15.4 | 11-deoxycortisol + reduced adrenal ferredoxin + O2 |
CYP11B1 |
1.14.15.4 | 11-deoxycortisol + reduced adrenal ferredoxin + O2 |
deficiency of steroid 11-hydroxylase CYP11B1 due to mutations in the CYP11B1 gene causes congenital adrenal hyperplasia, a group of autosomal recessive disorders, overview |
1.14.15.4 | 16,17alpha-epoxyprogesterone + reduced adrenal ferredoxin + O2 |
- |
1.14.15.4 | 18-hydroxy-corticosterone + reduced adrenal ferredoxin + O2 |
18-hydroxylation, last 3 steps of pathway for aldosterone biosynthesis |
1.14.15.4 | 18-hydroxycorticosterone + reduced adrenal ferredoxin + O2 |
- |