EC Number | Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|---|
4.1.2.63 | peroxisome | - |
Mus musculus | 5777 | - |
EC Number | Metals/Ions | Comment | Organism | Structure |
---|---|---|---|---|
4.1.2.63 | Mg2+ | required | Mus musculus |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.1.2.63 | 2-hydroxyphytanoyl-CoA | Mus musculus | - |
pristanal + formyl-CoA | - |
? |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
4.1.2.63 | Mus musculus | Q9QXE0 | - |
- |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
4.1.2.63 | brain | - |
Mus musculus | - |
4.1.2.63 | hepatocyte | - |
Mus musculus | - |
4.1.2.63 | liver | - |
Mus musculus | - |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.1.2.63 | 2-hydroxyoctadecanoyl-CoA | - |
Mus musculus | heptadecanal + formyl-CoA | - |
? | |
4.1.2.63 | 2-hydroxyphytanoyl-CoA | - |
Mus musculus | pristanal + formyl-CoA | - |
? |
EC Number | Subunits | Comment | Organism |
---|---|---|---|
4.1.2.63 | homotetramer | 4 * 60000, calculated from amino acid sequence | Mus musculus |
EC Number | Synonyms | Comment | Organism |
---|---|---|---|
4.1.2.63 | 2-hydroxyacyl-CoA lyase | - |
Mus musculus |
4.1.2.63 | HACL1 | - |
Mus musculus |
EC Number | Cofactor | Comment | Organism | Structure |
---|---|---|---|---|
4.1.2.63 | thiamine diphosphate | - |
Mus musculus |
EC Number | General Information | Comment | Organism |
---|---|---|---|
4.1.2.63 | malfunction | enzyme deficiency is not associated with a severe phenotype, but in combination with phytanic acid intake it might present with phytanic acid elevation and resemble a Refsum like disorder | Mus musculus |