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Literature summary extracted from

  • Wanders, R.
    L-2-hydroxyglutaric aciduria normal L-2-hydroxyglutarate dehydrogenase activity in liver from two new patients (1997), J. Inherit. Metab. Dis., 20, 725-726 .
    View publication on PubMed

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
1.1.99.2 (S)-2-hydroxyglutarate + NAD+ Homo sapiens
-
2-oxoglutarate + NADH + H+
-
?

Organism

EC Number Organism UniProt Comment Textmining
1.1.99.2 Homo sapiens
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
1.1.99.2 liver
-
Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.1.99.2 (S)-2-hydroxyglutarate + NAD+
-
Homo sapiens 2-oxoglutarate + NADH + H+
-
?

Synonyms

EC Number Synonyms Comment Organism
1.1.99.2 L-2-hydroxyglutarate dehydrogenase
-
Homo sapiens

Cofactor

EC Number Cofactor Comment Organism Structure
1.1.99.2 NAD+ dependent on Homo sapiens