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Literature summary extracted from

  • Yadav, A.K.; Shen, D.L.; Shan, X.; He, X.; Kermode, A.R.; Vocadlo, D.J.
    Fluorescence-quenched substrates for live cell imaging of human glucocerebrosidase activity (2015), J. Am. Chem. Soc., 137, 1181-1189 .
    View publication on PubMed

Inhibitors

EC Number Inhibitors Comment Organism Structure
3.2.1.45 AT3375
-
Homo sapiens
3.2.1.45 conduritol B epoxide
-
Homo sapiens

Localization

EC Number Localization Comment Organism GeneOntology No. Textmining
3.2.1.45 lysosome
-
Homo sapiens 5764
-

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.45 Homo sapiens P04062
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.45 fibroblast
-
Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.45 3-amido-(Black Hole Quencher 2)-6-methoxytriazolyl-1'-ethyl-3'-amido-(boron-dipyrromethene 576/589) beta-D-glucopyranoside + H2O
-
Homo sapiens 6-methoxytriazolyl-1'-ethyl-3'-amido-(boron-dipyrromethene 576/589) beta-D-glucopyranoside + Black Hole Quencher 2-N-(3-hydroxypropyl)butanamide
-
?
3.2.1.45 3-amido-[4-[[4-(dimethylamino)phenyl]azo]-benzoic acid]-L-6-methoxytriazol-5-[(2-azidoethyl)amino]naphthalene-1-sulfonic acid beta-D-glucopyranoside + H2O
-
Homo sapiens 6-O-[(1-[2-[(5-sulfonaphthalen-1-yl)amino]ethyl]-1H-1,2,3-triazol-4-yl)methyl]-beta-D-glucopyranose + 4-[(Z)-[4-(dimethylamino)phenyl]diazenyl]-N-(3-hydroxypropyl)benzamide
-
?
3.2.1.45 4-methylumbelliferyl beta-D-glucoside + H2O
-
Homo sapiens 4-methylumbelliferone + beta-D-glucose
-
?

Synonyms

EC Number Synonyms Comment Organism
3.2.1.45 acid beta-glucosidase
-
Homo sapiens
3.2.1.45 GBA1
-
Homo sapiens
3.2.1.45 Gcase
-
Homo sapiens
3.2.1.45 glucocerebrosidase
-
Homo sapiens

pH Optimum

EC Number pH Optimum Minimum pH Optimum Maximum Comment Organism
3.2.1.45 5.5
-
-
Homo sapiens

General Information

EC Number General Information Comment Organism
3.2.1.45 malfunction enzyme deficiency leads to abnormal accumulation of glucosyl ceramide in lysosomes and the development of the lysosomal storage disease known as Gauchers disease Homo sapiens