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Literature summary extracted from

  • Ou, L.; Herzog, T.L.; Wilmot, C.M.; Whitley, C.B.
    Standardization of alpha-L-iduronidase enzyme assay with Michaelis-Menten kinetics (2014), Mol. Genet. Metab., 111, 113-115.
    View publication on PubMedView publication on EuropePMC

Protein Variants

EC Number Protein Variants Comment Organism
3.2.1.76 additional information construction of knockout mice from C57BL/6 parents Mus musculus

KM Value [mM]

EC Number KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
3.2.1.76 additional information
-
additional information Michaelis-Menten kinetics Mus musculus

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.76 Mus musculus
-
gene IDUA
-
3.2.1.76 Mus musculus C57BL/6
-
gene IDUA
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.76 liver heterozygous mice Mus musculus
-

Specific Activity [micromol/min/mg]

EC Number Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
3.2.1.76 0.000005 0.00011 activity levels from the same specimens of heterozygous mice vary greatly with different substrate concentrations of 4-methylumbelliferyl-alpha-L-iduronide, comparison of activities in livers at 15 different concentrations, overview. pH and temperature not specified in the publication Mus musculus

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.76 4-methylumbelliferyl-alpha-L-iduronide + H2O
-
Mus musculus 4-methylumbelliferol + alpha-L-iduronic acid
-
?
3.2.1.76 4-methylumbelliferyl-alpha-L-iduronide + H2O
-
Mus musculus C57BL/6 4-methylumbelliferol + alpha-L-iduronic acid
-
?

Synonyms

EC Number Synonyms Comment Organism
3.2.1.76 alpha-L-iduronidase
-
Mus musculus
3.2.1.76 IDUA
-
Mus musculus

Temperature Optimum [°C]

EC Number Temperature Optimum [°C] Temperature Optimum Maximum [°C] Comment Organism
3.2.1.76 22 37 assay at Mus musculus