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Literature summary extracted from

  • Wang, D.; Worsham, D.N.; Pan, D.
    Co-expression of MGMT(P140K) and alpha-L-iduronidase in primary hepatocytes from mucopolysaccharidosis type I mice enables efficient selection with metabolic correction (2008), J. Gene Med., 10, 249-259.
    View publication on PubMedView publication on EuropePMC

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.76 Mus musculus
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-
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Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.76 AML-12 cell
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Mus musculus
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3.2.1.76 hepatocyte
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Mus musculus
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Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.76 4-methylumbelliferyl-alpha-L-iduronide + H2O
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Mus musculus 4-methylumbelliferone + alpha-L-iduronic acid
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Synonyms

EC Number Synonyms Comment Organism
3.2.1.76 alpha-L-iduronidase
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Mus musculus
3.2.1.76 IDUA
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Mus musculus