Any feedback?
Please rate this page
(literature.php)
(0/150)

BRENDA support

Literature summary extracted from

  • Arfi, A.; Zisling, R.; Richard, E.; Batista, L.; Poenaru, L.; Futerman, A.H.; Caillaud, C.
    Reversion of the biochemical defects in murine embryonic Sandhoff neurons using a bicistronic lentiviral vector encoding hexosaminidase alpha and beta (2006), J. Neurochem., 96, 1572-1579.
    View publication on PubMed

Application

EC Number Application Comment Organism
3.2.1.52 medicine therapeutic approach for Sandhoff disease Mus musculus

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.52 Mus musculus
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.52 neuronal cell line
-
Mus musculus
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.52 p-nitrophenyl-N-acetyl-D-glucosamine + H2O
-
Mus musculus N-acetyl-D-glucosamine + p-nitrophenol
-
?

Synonyms

EC Number Synonyms Comment Organism
3.2.1.52 beta-hexosaminidase
-
Mus musculus
3.2.1.52 hexosaminidase A
-
Mus musculus
3.2.1.52 hexosaminidase B
-
Mus musculus

pH Optimum

EC Number pH Optimum Minimum pH Optimum Maximum Comment Organism
3.2.1.52 4.5
-
-
Mus musculus