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Literature summary extracted from

  • Dekker, P.B.D.; Hogendoorn, P.C.W.; Kuipers-Dijkshoorn, N.; Prins, F.A.; van Duinen, S.G.; Taschner, P.E.M.; van der Mey, A.G.L.; Cornelisse, C.J.
    SDHD mutations in head and neck paragangliomas result in destabilization of complex II in the mitochondrial respiratory chain with loss of enzymatic activity and abnormal mitochondrial morphology (2003), J. Pathol., 201, 480-486.
    View publication on PubMed

Localization

EC Number Localization Comment Organism GeneOntology No. Textmining
1.3.5.1 mitochondrion
-
Homo sapiens 5739
-

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
1.3.5.1 succinate + ubiquinone Homo sapiens
-
fumarate + ubiquinol
-
?

Organism

EC Number Organism UniProt Comment Textmining
1.3.5.1 Homo sapiens
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
1.3.5.1 additional information loss of SDH activity in chief cells is found in the majority, i.e. 90%, of head and neck paragaliomas Homo sapiens
-
1.3.5.1 myocardium
-
Homo sapiens
-
1.3.5.1 renal tubule epithelium Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.3.5.1 succinate + ubiquinone
-
Homo sapiens fumarate + ubiquinol
-
?

Synonyms

EC Number Synonyms Comment Organism
1.3.5.1 SDH
-
Homo sapiens