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Literature summary extracted from

  • Korman, S.H.; Andresen, B.S.; Zeharia, A.; Gutman, A.; Boneh, A.; Pitt, J.J.
    2-Ethylhydracrylic aciduria in short/branched-chain acyl-CoA dehydrogenase deficiency: application to diagnosis and implications for the R-pathway of isoleucine oxidation (2005), Clin. Chem., 51, 610-617.
    View publication on PubMed

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
1.3.8.5 (R)-2-methylbutanoyl-CoA + electron-transfer flavoprotein Homo sapiens involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+
-
 ?
1.3.8.5 (S)-2-methylbutanoyl-CoA + electron-transfer flavoprotein Homo sapiens involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+
-
 ?
1.3.8.5 additional information Homo sapiens enzyme deficiency causes 2-ethylhydracrylic aciduria with excretion f 2-methylbutyrylglycine ?
-
 ?

Organism

EC Number Organism UniProt Comment Textmining
1.3.8.5 Homo sapiens
-
-
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.3.8.5 (R)-2-methylbutanoyl-CoA + electron-transfer flavoprotein
-
 Homo sapiens 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+ i.e. ethylacrylyl-CoA ?
1.3.8.5 (R)-2-methylbutanoyl-CoA + electron-transfer flavoprotein involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers Homo sapiens 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+
-
 ?
1.3.8.5 (S)-2-methylbutanoyl-CoA + electron-transfer flavoprotein
-
 Homo sapiens 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+ i.e. tiglyl-CoA ?
1.3.8.5 (S)-2-methylbutanoyl-CoA + electron-transfer flavoprotein involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers Homo sapiens 2-methylbut-2-enoyl-CoA + reduced electron-transfer flavoprotein + H+
-
 ?
1.3.8.5 additional information enzyme deficiency causes 2-ethylhydracrylic aciduria with excretion f 2-methylbutyrylglycine Homo sapiens ?
-
 ?

Synonyms

EC Number Synonyms Comment Organism
1.3.8.5 SBCADD
-
 Homo sapiens
1.3.8.5 short/branched chain acyl-CoA dehydrogenase
-
 Homo sapiens