EC Number | Cloned (Comment) | Organism |
---|---|---|
4.3.2.1 | cloning of cDNA | Homo sapiens |
EC Number | Protein Variants | Comment | Organism |
---|---|---|---|
4.3.2.1 | additional information | the mutations E86A and R113W identified on separate alleles are most likely to determine ASL-deficiency in a severely affected patient with neonatal onset of the disease | Homo sapiens |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.3.2.1 | (Nomega-L-arginino)succinate | Homo sapiens | - |
fumarate + L-arginine | - |
r |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
4.3.2.1 | Homo sapiens | - |
- |
- |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
4.3.2.1 | liver | - |
Homo sapiens | - |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
4.3.2.1 | (Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
? | |
4.3.2.1 | (Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
r |
EC Number | Synonyms | Comment | Organism |
---|---|---|---|
4.3.2.1 | ASL | - |
Homo sapiens |