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Literature summary extracted from

  • Tavazzi, D.; Di Montemuros, F.M.; Fargion, S.; Fracanzani, A.L.; Fiorelli, G.; Cappellini, M.D.
    Levels of uroporphyrinogen decarboxylase (URO-D) in erythrocytes of Italian porphyria cutanea tarda patients (2002), Cell. Mol. Biol., 48, 27-32.
    View publication on PubMed

Application

EC Number Application Comment Organism
4.1.1.37 medicine PCT is a human metabolic disorder, due to the acquired or genetic impairment of uroporphyrinogen decarboxylase activity Homo sapiens

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
4.1.1.37 Uroporphyrinogen III Homo sapiens fifth enzyme of the heme biosynthetic pathway Coproporphyrinogen III + 4 CO2
-
?

Organism

EC Number Organism UniProt Comment Textmining
4.1.1.37 Homo sapiens
-
human, italian porphyria cutanea tarda patients
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4.1.1.37 Uroporphyrinogen III
-
Homo sapiens Coproporphyrinogen III + 4 CO2
-
?
4.1.1.37 Uroporphyrinogen III fifth enzyme of the heme biosynthetic pathway Homo sapiens Coproporphyrinogen III + 4 CO2
-
?

Synonyms

EC Number Synonyms Comment Organism
4.1.1.37 URO-D
-
Homo sapiens
4.1.1.37 uroporphyrinogen decarboxylase
-
Homo sapiens