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Literature summary extracted from

  • Whiting, M.J.; Elliott, W.H.
    Purification and properties of solubilized mitochondrial delta-aminolevulinic acid synthetase and comparison with the cytosol enzyme (1972), J. Biol. Chem., 247, 6818-6826.
    View publication on PubMed

Inhibitors

EC Number Inhibitors Comment Organism Structure
2.3.1.37 hemin
-
Cavia porcellus
2.3.1.37 hemin feed-back inhibition Rattus norvegicus

KM Value [mM]

EC Number KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
2.3.1.37 0.001 0.01 pyridoxal 5'-phosphate
-
Rattus norvegicus
2.3.1.37 0.2
-
succinyl-CoA
-
Rattus norvegicus
2.3.1.37 19
-
glycine
-
Rattus norvegicus

Localization

EC Number Localization Comment Organism GeneOntology No. Textmining
2.3.1.37 cytosol
-
Rattus norvegicus 5829
-
2.3.1.37 mitochondrion
-
Cavia porcellus 5739
-
2.3.1.37 mitochondrion
-
Rattus norvegicus 5739
-
2.3.1.37 additional information
-
Cavia porcellus
-
-
2.3.1.37 additional information processing of enzyme during to targeting to subcellular compartments Rattus norvegicus
-
-

Molecular Weight [Da]

EC Number Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
2.3.1.37 77000
-
mitochondria, gel filtration Rattus norvegicus
2.3.1.37 178000
-
cytosol, gel filtration Rattus norvegicus

Organism

EC Number Organism UniProt Comment Textmining
2.3.1.37 Cavia porcellus
-
-
-
2.3.1.37 Rattus norvegicus
-
2 isoforms in cytosol and mitochondria
-

Purification (Commentary)

EC Number Purification (Comment) Organism
2.3.1.37
-
Cavia porcellus
2.3.1.37 partial Rattus norvegicus

Source Tissue

EC Number Source Tissue Comment Organism Textmining
2.3.1.37 liver
-
Cavia porcellus
-
2.3.1.37 liver porphyric Rattus norvegicus
-

Storage Stability

EC Number Storage Stability Organism
2.3.1.37 -15°C, loss of 25% activity within 10 days Rattus norvegicus
2.3.1.37 4°C, loss of 40% activity within 10 days Rattus norvegicus

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
2.3.1.37 succinyl-CoA + glycine
-
Cavia porcellus 5-aminolevulinate + CoA + CO2
-
?
2.3.1.37 succinyl-CoA + glycine
-
Rattus norvegicus 5-aminolevulinate + CoA + CO2
-
?

Cofactor

EC Number Cofactor Comment Organism Structure
2.3.1.37 pyridoxal 5'-phosphate
-
Cavia porcellus
2.3.1.37 pyridoxal 5'-phosphate
-
Rattus norvegicus