Any feedback?
Please rate this page
(literature.php)
(0/150)

BRENDA support

Literature summary extracted from

  • Ribeiro, M.G.; Pinto, R.A.; Dos Santos, M.R.; Maia, M.; Sa Miranda, M.C.
    Biochemical characterization of beta-acetylhexosaminidase in different biological specimens from eleven patients with GM2-gangliosidosis B1 variant (1991), J. Inherit. Metab. Dis., 14, 715-720.
    View publication on PubMed

Localization

EC Number Localization Comment Organism GeneOntology No. Textmining
3.2.1.52 lysosome
-
Homo sapiens 5764
-

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
3.2.1.52 N-acetyl-beta-D-hexosaminides + H2O Homo sapiens
-
N-acetyl-D-hexosamines
-
?

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.52 Homo sapiens
-
patients with GM2-gangliosidosis B1 variant from the north of Portugal
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.52 fibroblast skin fibroblast Homo sapiens
-
3.2.1.52 leukocyte from peripheral blood Homo sapiens
-
3.2.1.52 lymphoblast
-
Homo sapiens
-
3.2.1.52 serum
-
Homo sapiens
-

Specific Activity [micromol/min/mg]

EC Number Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
3.2.1.52 additional information
-
-
Homo sapiens

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.52 4-methylumbelliferyl-2-acetamido-2-deoxy-beta-D-glucopyranoside + H2O
-
Homo sapiens 4-methylumbelliferone + 2-acetamido-2-deoxy-beta-D-glucopyranoside
-
?
3.2.1.52 4-methylumbelliferyl-2-acetamido-2-deoxy-beta-D-glucopyranoside-6-sulfate + H2O
-
Homo sapiens 4-methylumbelliferone + 2-acetamido-2-deoxy-beta-D-glucopyranoside-6-sulfate
-
?
3.2.1.52 N-acetyl-beta-D-hexosaminides + H2O
-
Homo sapiens N-acetyl-D-hexosamines
-
?