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Literature summary extracted from

  • Roe, C.R.; Millington, D.S.; Norwood, D.L.; Sprecher, H.; Mohammed, B.S.; Nada, M.; Schulz, H.; McVie, R.
    2,4-Dienolyl-coenzyme A reductase deficiency: a possible new disorder of fatty acid oxidation (1990), J. Clin. Invest., 85, 1703-1707.
    View publication on PubMedView publication on EuropePMC

Inhibitors

EC Number Inhibitors Comment Organism Structure
1.3.1.124 lysine slight inhibition Homo sapiens

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
1.3.1.124 2-trans,4-cis-decadienoylcarnitine + ? Homo sapiens abnormal unsaturated fatty acid oxidation ?
-
?

Organism

EC Number Organism UniProt Comment Textmining
1.3.1.124 Homo sapiens
-
female, in the neonatal period
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
1.3.1.124 liver soluble tissue extract for the enzyme assays Homo sapiens
-
1.3.1.124 muscle soluble tissue extract for the enzyme assays Homo sapiens
-
1.3.1.124 urine source of the natural substrate 2-trans,4cis-decadienoylcarnitine Homo sapiens
-

Specific Activity [micromol/min/mg]

EC Number Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
1.3.1.124 0.003
-
2-trans,4-trans-decadienoyl-CoA, NADPH, muscle Homo sapiens
1.3.1.124 0.0046
-
2-trans,4-cis-decadienoyl-CoA, NADPH, muscle Homo sapiens
1.3.1.124 0.0084
-
2-trans,4-trans-decadienoyl-CoA, NADPH, liver Homo sapiens
1.3.1.124 0.013
-
2-trans,4-cis-decadienoyl-CoA, NADPH, liver Homo sapiens

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.3.1.124 2-trans,4-cis-decadienoyl-CoA + NADPH
-
Homo sapiens 3-trans-decenoyl-CoA + NADP+
-
?
1.3.1.124 2-trans,4-cis-decadienoylcarnitine + ? abnormal unsaturated fatty acid oxidation Homo sapiens ?
-
?
1.3.1.124 2-trans,4-trans-decadienoyl-CoA + NADPH
-
Homo sapiens 3-decenoyl-CoA + NADP+
-
?

Synonyms

EC Number Synonyms Comment Organism
1.3.1.124 2,4-dienoyl-CoA reductase
-
Homo sapiens

Cofactor

EC Number Cofactor Comment Organism Structure
1.3.1.124 NADPH
-
Homo sapiens