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Literature summary extracted from

  • Gibson, K.M.
    3-Methylglutaconyl-coenzyme-A hydratase deficiency: a new case (1992), J. Inherit. Metab. Dis., 15, 363-366.
    View publication on PubMed

Organism

EC Number Organism UniProt Comment Textmining
4.2.1.18 Homo sapiens
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patients with methylglutaconyl-CoA hydratase deficiency with diverse clinical syndromes
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Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4.2.1.18 (S)-3-hydroxy-3-methylglutaryl-CoA
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Homo sapiens trans-3-methylglutaconyl-CoA + H2O
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