Any feedback?
Please rate this page
(literature.php)
(0/150)

BRENDA support

Literature summary extracted from

  • Mononen, I.; Mononen, T.; Ylikangas, P.; Kaartinen, V.; Savolainen, K.
    Enzymatic diagnosis of aspartylglycosaminuria by fluorometric assay of glycosylasparaginase in serum, plasma, or lymphocytes (1994), Clin. Chem., 40, 385-388.
    View publication on PubMed

Application

EC Number Application Comment Organism
3.5.1.26 medicine fluorometric assay in blood samples allows specific detection of the enzyme defect in aspartylglycosaminuria patients Homo sapiens

Organism

EC Number Organism UniProt Comment Textmining
3.5.1.26 Homo sapiens
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.5.1.26 lymphocyte
-
Homo sapiens
-
3.5.1.26 plasma
-
Homo sapiens
-
3.5.1.26 serum
-
Homo sapiens
-

Specific Activity [micromol/min/mg]

EC Number Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
3.5.1.26 0.02
-
in serum and plasma Homo sapiens
3.5.1.26 0.24
-
in lymphocytes Homo sapiens

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.5.1.26 L-aspartic acid beta-(7-amido-4-methylcoumarin) + H2O
-
Homo sapiens 7-amino-4-methylcoumarin + L-aspartate
-
?

Synonyms

EC Number Synonyms Comment Organism
3.5.1.26 glycosylasparaginase
-
Homo sapiens