Any feedback?
Please rate this page
(literature.php)
(0/150)

BRENDA support

Literature summary extracted from

  • Ahadeff, J.A; Andrews-Smith, G.L.
    Purification and characterization of alpha-L-fucosidase from the liver of a fucosidosis patient (1980), Biochem. J., 187, 45-51.
    View publication on PubMedView publication on EuropePMC

KM Value [mM]

EC Number KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
3.2.1.51 0.14
-
4-methylumbelliferyl-alpha-L-fucopyranoside 4-5fold increase in fucosidosis patients Homo sapiens

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.51 Homo sapiens
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.51 liver characterization of alpha-fucosidase from fucosidosis patients Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.51 4-methylumbelliferyl-alpha-L-fucopyranoside + H2O
-
Homo sapiens 4-methylumbelliferone + alpha-L-fucose
-
?

Temperature Stability [°C]

EC Number Temperature Stability Minimum [°C] Temperature Stability Maximum [°C] Comment Organism
3.2.1.51 50 55 greatly decreased thermostability in fucosidosis patients Homo sapiens