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Literature summary extracted from

  • Kobayashi, T.; Shinnoh, N.; Kuroiwa, Y.
    Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy (1986), Biochim. Biophys. Acta, 879, 215-220.
    View publication on PubMed

Activating Compound

EC Number Activating Compound Comment Organism Structure
3.2.1.46 taurocholate
-
Mus musculus
3.2.1.46 taurocholate
-
Homo sapiens

Application

EC Number Application Comment Organism
3.2.1.46 medicine twitcher mouse, a model for globoid cell leucodystrophy Mus musculus
3.2.1.46 medicine enzyme deficiency in globoid cell leucodystrophy or Krabbe disease Homo sapiens

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O Mus musculus
-
?
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O Homo sapiens
-
?
-
?

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.46 Homo sapiens
-
-
-
3.2.1.46 Mus musculus
-
twitcher mouse
-

Purification (Commentary)

EC Number Purification (Comment) Organism
3.2.1.46 partially Mus musculus

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.46 liver
-
Mus musculus
-
3.2.1.46 liver
-
Homo sapiens
-
3.2.1.46 placenta
-
Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus D-galactose + N-acylsphingosine
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens D-galactose + N-acylsphingosine
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus ?
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens ?
-
?
3.2.1.46 galactocerebroside + H2O
-
Mus musculus D-galactose + N-acylceramide
-
?
3.2.1.46 galactocerebroside + H2O
-
Homo sapiens D-galactose + N-acylceramide
-
?