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Literature summary extracted from

  • Matsuda, Y.; Tsuji, A.; Katunuma, N.; Hayashi, M.; Takahashi, Y.
    Studies on liver argininosuccinate synthetase in a patient with citrullinemia and in normal subjects (1979), J. Biochem., 85, 191-195.
    View publication on PubMed

General Stability

EC Number General Stability Organism
6.3.4.5 argininosuccinate stabilizes against heat treatment Homo sapiens

KM Value [mM]

EC Number KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
6.3.4.5 0.029
-
L-Asp normal liver and from patients with citrullinemia Homo sapiens
6.3.4.5 0.03
-
L-citrulline normal liver Homo sapiens
6.3.4.5 0.18
-
ATP normal liver and from patients with citrullinemia Homo sapiens

Molecular Weight [Da]

EC Number Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
6.3.4.5 185000
-
sucrose density gradient centrifugation Homo sapiens

Organism

EC Number Organism UniProt Comment Textmining
6.3.4.5 Homo sapiens
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
6.3.4.5 liver normal and from patients with citrullinemia Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
6.3.4.5 ATP + L-citrulline + L-Asp
-
Homo sapiens AMP + diphosphate + L-argininosuccinate
-
?

Temperature Stability [°C]

EC Number Temperature Stability Minimum [°C] Temperature Stability Maximum [°C] Comment Organism
6.3.4.5 additional information
-
argininosuccinate stabilizes against heat treatment Homo sapiens
6.3.4.5 50
-
7 min, enzyme from normal liver and from patients with citrullinemia, in presence of 10 mM argininosuccinate, about 10% loss of activity Homo sapiens
6.3.4.5 50
-
7 min, enzyme from patients with citrullinemia, in absence of argininosuccinate, 95% loss of activity Homo sapiens
6.3.4.5 50
-
7 min, enzyme from normal liver, in absence of argininosuccinate, about 65% loss of activity Homo sapiens