EC Number | Activating Compound | Comment | Organism | Structure |
---|---|---|---|---|
3.2.1.45 | saposin-C | activation varies depending on mutation | Homo sapiens | |
3.2.1.45 | sodium taurocholate | - |
Homo sapiens |
EC Number | Application | Comment | Organism |
---|---|---|---|
3.2.1.45 | medicine | Gaucher disease, sphingolipoidose | Homo sapiens |
EC Number | KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|---|
3.2.1.45 | 2.1 | 3.7 | 4-methylumbelliferyl-beta-D-glucopyranoside | different patients | Homo sapiens |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
3.2.1.45 | glucocerebroside + H2O | Homo sapiens | - |
glucose + ceramide | - |
? |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
3.2.1.45 | Homo sapiens | - |
normal and Gaucher disease enzyme | - |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
3.2.1.45 | fibroblast | skin fibroblasts in culture | Homo sapiens | - |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
3.2.1.45 | 4-methylumbelliferyl-beta-D-glucopyranoside + H2O | - |
Homo sapiens | methylumbelliferone + glucose | - |
? | |
3.2.1.45 | 6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosyl 1-O-beta-D-glucoside + H2O | NBD-glucocerebroside | Homo sapiens | D-glucose + 6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosine | - |
? | |
3.2.1.45 | 6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosyl 1-O-beta-D-glucoside + H2O | complexed with bovine serum albumin | Homo sapiens | D-glucose + 6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosine | - |
? | |
3.2.1.45 | glucocerebroside + H2O | - |
Homo sapiens | glucose + ceramide | - |
? |