Cloned (Comment) | Organism |
---|---|
expression in Escherichia coli and COS-7 cells | Homo sapiens |
Protein Variants | Comment | Organism |
---|---|---|
A398D | no activity, 15.55 of wild-type activity if coexpressed with Q286R | Homo sapiens |
D87G | no activity, 35.2% of wild-type activity if coexpressed with Q286R | Homo sapiens |
M360T | no actiivty, 10% of wild-type activity if coexpressed with Q286R | Homo sapiens |
Q286R | 3% of wild-type activity | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.12 | - |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | - |
Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | Homo sapiens | - |
fumarate + L-arginine | - |
r |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
ASL deficiency results in the autosomal, recessive disorder argininosuccinic aciduria | - |
Purification (Comment) | Organism |
---|---|
recombinant ASL | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
? | |
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
r | |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | - |
Homo sapiens | ? | - |
? |
Synonyms | Comment | Organism |
---|---|---|
ASL | - |
Homo sapiens |
Turnover Number Minimum [1/s] | Turnover Number Maximum [1/s] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
34.5 | - |
N,N'-bis(tert-butoxycarbonyl)-5-[(3-aminopropyl)amino]pentan-1-ol | - |
Homo sapiens |