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Literature summary for 3.5.1.26 extracted from

  • Mononen, I.; Mononen, T.; Ylikangas, P.; Kaartinen, V.; Savolainen, K.
    Enzymatic diagnosis of aspartylglycosaminuria by fluorometric assay of glycosylasparaginase in serum, plasma, or lymphocytes (1994), Clin. Chem., 40, 385-388.
    View publication on PubMed

Application

Application Comment Organism
medicine fluorometric assay in blood samples allows specific detection of the enzyme defect in aspartylglycosaminuria patients Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
lymphocyte
-
Homo sapiens
-
plasma
-
Homo sapiens
-
serum
-
Homo sapiens
-

Specific Activity [micromol/min/mg]

Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
0.02
-
in serum and plasma Homo sapiens
0.24
-
in lymphocytes Homo sapiens

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
L-aspartic acid beta-(7-amido-4-methylcoumarin) + H2O
-
Homo sapiens 7-amino-4-methylcoumarin + L-aspartate
-
?

Synonyms

Synonyms Comment Organism
glycosylasparaginase
-
Homo sapiens