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Literature summary for 3.4.14.9 extracted from

  • Chang, M.; Cooper, J.D.; Sleat, D.E.; Cheng, S.H.; Dodge, J.C.; Passini, M.A.; Lobel, P.; Davidson, B.L.
    Intraventricular enzyme replacement improves disease phenotypes in a mouse model of late infantile neuronal ceroid lipofuscinosis (2008), Mol. Ther., 16, 649-656.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
expressed in Chinese hamster ovary cells Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
lysosome
-
Homo sapiens 5764
-

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Purification (Commentary)

Purification (Comment) Organism
Sepharose 4 FF column chromatography and Blue Sepharose column chromatography Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining
brain
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
Ala-Ala-Phe-7-amido-4-methylcoumarin + H2O
-
Homo sapiens Ala-Ala-Phe + 7-amino-4-methylcoumarin
-
?

Synonyms

Synonyms Comment Organism
Tpp1
-
Homo sapiens
tripeptidyl peptidase 1
-
Homo sapiens