Inhibitors | Comment | Organism | Structure |
---|---|---|---|
1-deoxynojirimycin | - |
Homo sapiens | |
alkyl amines | - |
Homo sapiens | |
Alkyl beta-glucosides | - |
Homo sapiens | |
N-butyl-1-deoxynojirimycin | - |
Homo sapiens | |
N-decyl-1-deoxynojirimycin | - |
Homo sapiens | |
N-dodecyl-1-deoxynojirimycin | - |
Homo sapiens | |
N-methyl-1-deoxynojirimycin | - |
Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.014 | - |
D-glucosyl-N-methylsphingosine | - |
Homo sapiens | |
0.02 | - |
D-glucosyl-N-propylsphingosine | - |
Homo sapiens | |
0.028 | - |
stearylglucosyl ceramide | - |
Homo sapiens | |
0.03 | - |
6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexanoyl-2-N-sphingosyl 1-O-beta-D-glucoside | - |
Homo sapiens | |
0.032 | - |
D-glucosyl-N-ethylsphingosine | - |
Homo sapiens | |
0.033 | - |
D-glucosyl-N-octylsphingosine | - |
Homo sapiens | |
0.034 | - |
palmitylglucosyl ceramide | - |
Homo sapiens | |
0.042 | - |
D-glucosyl-N-butylsphingosine | - |
Homo sapiens | |
0.05 | - |
12(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosyl 1-O-beta-D-glucoside | - |
Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
glucocerebroside + H2O | Homo sapiens | - |
glucose + ceramide | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
normal and Gaucher disease enzyme | - |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
placenta | - |
Homo sapiens | - |
spleen | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
12(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminododecanoyl-2-N-sphingosyl 1-O-beta-D-glucoside + H2O | - |
Homo sapiens | D-glucose + 12(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminododecanoyl-2-N-sphingosine | - |
? | |
6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosyl 1-O-beta-D-glucoside + H2O | NBD-glucocerebroside | Homo sapiens | D-glucose + 6(N-methyl-N-(7-nitrobenz-2-oxa-1,3-diazol-4-yl))aminohexyl-2-N-sphingosine | - |
? | |
D-glucosyl-N-butylsphingosine + H2O | - |
Homo sapiens | D-glucose + N-butylsphingosine | - |
? | |
D-glucosyl-N-ethylsphingosine + H2O | - |
Homo sapiens | D-glucose + N-ethylsphingosine | - |
? | |
D-glucosyl-N-methylsphingosine + H2O | - |
Homo sapiens | D-glucose + N-methylsphingosine | - |
? | |
D-glucosyl-N-octylsphingosine + H2O | - |
Homo sapiens | D-glucose + N-octylsphingosine | - |
? | |
D-glucosyl-N-propylsphingosine + H2O | - |
Homo sapiens | D-glucose + N-propylsphingosine | - |
? | |
glucocerebroside + H2O | - |
Homo sapiens | glucose + ceramide | - |
? | |
N-stearoylglucosyl ceramide + H2O | - |
Homo sapiens | D-glucose + stearoylceramide | - |
? | |
palmitylglucosyl ceramide + H2O | - |
Homo sapiens | D-glucose + palmitylceramide | - |
? | |
stearylglucosyl ceramide + H2O | - |
Homo sapiens | D-glucose + stearylceramide | - |
? |