General Stability | Organism |
---|---|
neutral alpha-glucosidase is less stable than acid alpha-glucosidase | Homo sapiens |
Inhibitors | Comment | Organism | Structure |
---|---|---|---|
acarbose | - |
Homo sapiens | |
maltose | - |
Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
additional information | Homo sapiens | a severe form of enzyme deficiency causes the infantile Pompe disease | ? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
patients with infantile Pompe disease | - |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
blood | dried blood spot specimen from patients with infantile Pompe disease | Homo sapiens | - |
fibroblast | - |
Homo sapiens | - |
skin | fibroblasts | Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
additional information | - |
- |
Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl-alpha-D-glucopyranoside + H2O | - |
Homo sapiens | 4-methylumbelliferol + alpha-D-glucose | - |
? | |
additional information | a severe form of enzyme deficiency causes the infantile Pompe disease | Homo sapiens | ? | - |
? | |
additional information | development and evaluation of an assay method for enzyme detection in dried blood spot specimen from patients with infantile Pompe disease, overview | Homo sapiens | ? | - |
? |
Synonyms | Comment | Organism |
---|---|---|
acid alpha-glucosidase | - |
Homo sapiens |
maltase-glucoamylase | - |
Homo sapiens |
neutral alpha-glucosidase | - |
Homo sapiens |
Temperature Optimum [°C] | Temperature Optimum Maximum [°C] | Comment | Organism |
---|---|---|---|
37 | - |
assay at | Homo sapiens |
pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|
3.8 | - |
acid alpha-glucosidase assay at | Homo sapiens |
7 | - |
neutral alpha-glucosidase assay at | Homo sapiens |