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Literature summary for 3.1.6.14 extracted from

  • Di Ferrante, N.
    N-acetylglucosamine-6-sulfate sulfatase deficiency reconsidered (1980), Science, 210, 448.
    View publication on PubMed

Application

Application Comment Organism
medicine normal activity in patient G.G.,cell line GM 2243 Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
N-acetyl-D-glucosamine 6-sulfate units + H2O Homo sapiens in oligo-and monosaccharides derived from heparan sulfate and keratan sulfate N-acetyl-D-glucosamine units + sulfate
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
skin fibroblast in culture Homo sapiens
-
skin fibroblast fibroblast line GM 2243 Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
N-acetyl-D-glucosamine 6-sulfate units + H2O
-
Homo sapiens N-acetyl-D-glucosamine units + sulfate
-
?
N-acetyl-D-glucosamine 6-sulfate units + H2O in oligo-and monosaccharides derived from heparan sulfate and keratan sulfate Homo sapiens N-acetyl-D-glucosamine units + sulfate
-
?