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Literature summary for 2.1.4.1 extracted from

  • Carducci, C.; Birarelli, M.; Leuzzi, V.; Carducci, C.; Battini, R.; Cioni, G.; Antonozzi, I.
    Guanidinoacetate and creatine plus creatinine assessment in physiologic fluids: an effective diagnostic tool for the biochemical diagnosis of arginine:glycine amidinotransferase and guanidinoacetate methyltransferase deficiencies (2002), Clin. Chem., 48, 1772-1778.
    View publication on PubMed

Application

Application Comment Organism
medicine diagnostic tool for biochemical diagnosis of creatine metabolism disorders Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
L-arginine + glycine Homo sapiens
-
L-ornithine + guanidinoacetate
-
r

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
human
-

Source Tissue

Source Tissue Comment Organism Textmining
brain
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
canavanine + ornithine
-
Homo sapiens arginine + canaline
-
r
L-arginine + glycine
-
Homo sapiens L-ornithine + guanidinoacetate
-
r