EC Number |
Natural Substrates |
---|
2.4.1.62 | more |
mice heterozygous for a non-functional allele of UDPgalactose:ceramide-galactosyltransferase show decreased synthesis of galactosylceramide and sulfatide, which should reduce sulfatide storage and improve pathology in arylsulfatase A-deficient mice. The phenotypic and pathologic improvements in ASA-/- CGT+/- mice are significant but overall minor |
2.4.1.62 | more |
UDPgalactose:ceramide galactosyltransferase activity does not limit total galactosylceramide level. Tight control of UDP-galactose:ceramide galactosyltransferase expression is essential for myelin maintenance |
2.4.1.62 | UDP-galactose + asialo-GM2 |
i.e. Gg3 |
2.4.1.62 | UDP-galactose + ganglioside GA2 |
i.e. Cer-Glc-Gal-GalNAc |
2.4.1.62 | UDP-galactose + GD2 |
i.e. Cer-Glc-Gal-(GalNAc)(NeuNAc2) |
2.4.1.62 | UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine |
- |
2.4.1.62 | UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine |
key enzyme in the biosynthesis of the oligodendrocyte- and myelin-specific cerebrosides |
2.4.1.62 | UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine |
involved in biosynthesis of gangliosides |