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Literature summary extracted from

  • Wiederschain, G.; Raghavan, S.; Kolodny, E.
    Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-beta-D-galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease (1992), Clin. Chim. Acta, 205, 87-96.
    View publication on PubMed

Activating Compound

EC Number Activating Compound Comment Organism Structure
3.2.1.46 taurocholate in combination with oleic acid Mus musculus
3.2.1.46 taurocholate in combination with oleic acid Homo sapiens

Application

EC Number Application Comment Organism
3.2.1.46 medicine enzymatic diagnosis Mus musculus
3.2.1.46 medicine enzymatic diagnosis Homo sapiens

Inhibitors

EC Number Inhibitors Comment Organism Structure
3.2.1.46 6-hexadecanoylamino-4-methylbelliferyl-beta-D-galactopyranoside competitive Homo sapiens
3.2.1.46 6-hexadecanoylamino-4-methylbelliferyl-beta-D-galactopyranoside competitive Mus musculus

KM Value [mM]

EC Number KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
3.2.1.46 0.03
-
6-hexadecanoylamino-4-methylbelliferyl-beta-D-galactopyranoside taurocholate and oleic acid activated, in leukocytes Homo sapiens
3.2.1.46 0.04
-
6-hexadecanoylamino-4-methylbelliferyl-beta-D-galactopyranoside taurocholate and oleic acid activated, in fibroblasts Homo sapiens
3.2.1.46 0.15
-
6-hexadecanoylamino-4-methylbelliferyl-beta-D-galactopyranoside taurocholate and oleic acid activated Mus musculus

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O Mus musculus
-
?
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O Homo sapiens
-
?
-
?

Organism

EC Number Organism UniProt Comment Textmining
3.2.1.46 Homo sapiens
-
-
-
3.2.1.46 Mus musculus
-
twitcher mouse
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
3.2.1.46 brain
-
Homo sapiens
-
3.2.1.46 kidney
-
Mus musculus
-
3.2.1.46 leukocyte
-
Homo sapiens
-
3.2.1.46 skin fibroblast in culture Mus musculus
-
3.2.1.46 skin fibroblast in culture Homo sapiens
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
3.2.1.46 6-hexadecanoylamino-4-methylumbelliferyl-beta-D-galactopyranoside + H2O fluorogenic substrate Mus musculus 6-hexadecanoylamino-4-methylumbelliferone + beta-D-galactopyranose
-
?
3.2.1.46 6-hexadecanoylamino-4-methylumbelliferyl-beta-D-galactopyranoside + H2O fluorogenic substrate Homo sapiens 6-hexadecanoylamino-4-methylumbelliferone + beta-D-galactopyranose
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus D-galactose + N-acylsphingosine
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens D-galactose + N-acylsphingosine
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus ?
-
?
3.2.1.46 D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens ?
-
?
3.2.1.46 galactocerebroside + H2O
-
Mus musculus D-galactose + N-acylceramide
-
?
3.2.1.46 galactocerebroside + H2O
-
Homo sapiens D-galactose + N-acylceramide
-
?

pH Optimum

EC Number pH Optimum Minimum pH Optimum Maximum Comment Organism
3.2.1.46 4.5
-
taurocholate and oleic acid activated Mus musculus
3.2.1.46 4.5
-
taurocholate and oleic acid activated Homo sapiens