EC Number | Activating Compound | Comment | Organism | Structure |
---|---|---|---|---|
3.2.1.46 | Activator protein | purified from normal spleen | Homo sapiens | |
3.2.1.46 | cholate | - |
Homo sapiens | |
3.2.1.46 | phosphatidylcholine | from 0.02 mg to 0.1 mg | Homo sapiens | |
3.2.1.46 | phosphatidylinositol | from 0.02 mg to 0.05 mg | Homo sapiens | |
3.2.1.46 | phosphatidylserine | at 0.02 mg | Homo sapiens | |
3.2.1.46 | taurocholate | - |
Homo sapiens |
EC Number | Application | Comment | Organism |
---|---|---|---|
3.2.1.46 | medicine | enzyme deficiency in globoid cell leucodystrophy or Krabbe disease | Homo sapiens |
EC Number | KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|---|
3.2.1.46 | 0.11 | - |
galactosylsphingosine | without taurocholate | Homo sapiens | |
3.2.1.46 | 0.67 | - |
galactosylsphingosine | with taurocholate | Homo sapiens |
EC Number | Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
3.2.1.46 | D-galactosyl-N-acylsphingosine + H2O | Homo sapiens | - |
? | - |
? |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
3.2.1.46 | Homo sapiens | - |
- |
- |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
3.2.1.46 | brain | - |
Homo sapiens | - |
3.2.1.46 | skin fibroblast | in culture | Homo sapiens | - |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
3.2.1.46 | D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | D-galactose + N-acylsphingosine | - |
? | |
3.2.1.46 | D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | ? | - |
? | |
3.2.1.46 | galactocerebroside + H2O | - |
Homo sapiens | D-galactose + N-acylceramide | - |
? | |
3.2.1.46 | lactosylsphingosine + H2O | - |
Homo sapiens | lactose + sphingosine | - |
? | |
3.2.1.46 | psychosine + H2O | - |
Homo sapiens | D-galactose + sphingosine | - |
? |
EC Number | pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|---|
3.2.1.46 | 3.75 | - |
without taurocholate | Homo sapiens |
3.2.1.46 | 5.4 | - |
with taurocholate | Homo sapiens |