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Literature summary for 6.3.4.10 extracted from

  • Suzuki, Y.; Aoki, Y.; Ichida, Y.; Chiba, A.; Iwamatsu, T.; Kishini, T.; Matsubara, Y.; Narisawa, K.
    Isolation and characterization of mutations in the human holocarboxylase synthetase cDNA (1994), Nature Genet., 8, 122-128.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
-
Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)] eukaryota plays an essential role in biotin utilization ?
-
?
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)] Homo sapiens its deficiency causes biotin-responsive multiple carboxylase deficiency in humans ?
-
?

Organism

Organism UniProt Comment Textmining
eukaryota
-
-
-
Homo sapiens
-
-
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)]
-
eukaryota AMP + diphosphate + [propanoyl-CoA:carbon-dioxide ligase (ADP-forming)]
-
?
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)]
-
Homo sapiens AMP + diphosphate + [propanoyl-CoA:carbon-dioxide ligase (ADP-forming)]
-
?
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)] plays an essential role in biotin utilization eukaryota ?
-
?
ATP + biotin + apo-[propanoyl-CoA:carbon-dioxide ligase (ADP-forming)] its deficiency causes biotin-responsive multiple carboxylase deficiency in humans Homo sapiens ?
-
?