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Literature summary for 6.1.1.16 extracted from

  • Waterson, J.R.; Winter, W.P.; Schmickel, R.D.
    Cysteine activation in cultures cystinotic cells (1974), J. Clin. Invest., 54, 182-187.
    View publication on PubMedView publication on EuropePMC

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
additional information
-
additional information Km for ATP and tRNA is similar in normal and cystinotic cells Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
fibroblast cultured Homo sapiens
-
fibroblast from patients with cystinosis Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ATP + L-cysteine + tRNACys
-
Homo sapiens AMP + diphosphate + L-cysteinyl-tRNACys
-
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