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Literature summary for 5.4.99.2 extracted from

  • Ledley, F.D.; Lumetta, M.; Nguyen, P.N.; Kolhouse, J.F.; Allen, R.H.
    Molecular cloning of L-methylmalonyl-CoA mutase: gene transfer and analysis of mut cell lines (1988), Proc. Natl. Acad. Sci. USA, 85, 3518-3521.
    View publication on PubMedView publication on EuropePMC

Cloned(Commentary)

Cloned (Comment) Organism
-
Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrial matrix
-
Homo sapiens 5759
-

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
additional information Homo sapiens this enzyme is deficient in methylmalonic acidemia ?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
liver
-
Homo sapiens
-
placenta
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
(R)-2-methylmalonyl-CoA
-
Homo sapiens succinyl-CoA
-
?
additional information this enzyme is deficient in methylmalonic acidemia Homo sapiens ?
-
?