KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.00057 | - |
5-COOH-porphyrinogen I | enzyme from healthy individuals | Homo sapiens | |
0.001 | - |
5-COOH-porphyrinogen I | enzyme from patients with sporadic porphyria cutanea tarda | Homo sapiens | |
0.00133 | - |
Uroporphyrinogen I | enzyme from healthy individuals | Homo sapiens | |
0.00215 | - |
5-COOH-porphyrinogen I | enzyme from patients with familial porphyria cutanea tarda | Homo sapiens | |
0.00256 | - |
Uroporphyrinogen I | enzyme from patients with sporadic porphyria cutanea tarda | Homo sapiens | |
0.00533 | - |
Uroporphyrinogen I | enzyme from patients with familial porphyria cutanea tarda | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
additional information | Homo sapiens | the familial porphyria cutanea tarda is a genetically determined kinetic abnormality of uroporphyrinogen decarboxylase | ? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
erythrocyte | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
5-COOH-porphyrinogen I | - |
Homo sapiens | Coproporphyrinogen I + CO2 | - |
? | |
additional information | the familial porphyria cutanea tarda is a genetically determined kinetic abnormality of uroporphyrinogen decarboxylase | Homo sapiens | ? | - |
? | |
uroporphyrinogen I | - |
Homo sapiens | coproporphyrinogen I + 4 CO2 | - |
? |