Application | Comment | Organism |
---|---|---|
medicine | more than 80% of all patients with Zellweger syndrome, the most severe peroxisome biogenesis disorder, carry mutations in Pex1p or Pex6p | Homo sapiens |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
cytosol | - |
Homo sapiens | 5829 | - |
cytosol | - |
Saccharomyces cerevisiae | 5829 | - |
peroxisomal membrane | - |
Homo sapiens | 5778 | - |
peroxisomal membrane | - |
Saccharomyces cerevisiae | 5778 | - |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
ATP + H2O | Homo sapiens | - |
ADP + phosphate | - |
ir | |
ATP + H2O | Saccharomyces cerevisiae | - |
ADP + phosphate | - |
ir |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Saccharomyces cerevisiae | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
fibroblast | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
ATP + H2O | - |
Homo sapiens | ADP + phosphate | - |
ir | |
ATP + H2O | - |
Saccharomyces cerevisiae | ADP + phosphate | - |
ir |
Subunits | Comment | Organism |
---|---|---|
More | Pex1p and Pex6p are believed to form heterohexameric structures | Homo sapiens |
More | Pex1p and Pex6p are believed to form heterohexameric structures | Saccharomyces cerevisiae |
Synonyms | Comment | Organism |
---|---|---|
PAS1p | - |
Homo sapiens |
PAS1p | - |
Saccharomyces cerevisiae |
peroxisome-assembly ATPase | - |
Homo sapiens |
peroxisome-assembly ATPase | - |
Saccharomyces cerevisiae |
Pex1p | - |
Homo sapiens |
Pex1p | - |
Saccharomyces cerevisiae |
Pex6p | - |
Homo sapiens |
Pex6p | - |
Saccharomyces cerevisiae |