Application | Comment | Organism |
---|---|---|
medicine | plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.0158 | - |
biotinyl-monoiodotyramine | - |
Homo sapiens | |
0.027 | - |
biotinyl-di-iodotyramine | - |
Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | Homo sapiens | - |
? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Homo sapiens | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
human | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | - |
Homo sapiens | ? | - |
? | |
biotinyl-di-iodotyramine + H2O | - |
Homo sapiens | biotin + di-iodotyramine | - |
? | |
biotinyl-monoiodotyramine + H2O | radioactive assay for early diagnosis of biotinidase defiency in serum | Homo sapiens | biotin + monoiodotyramine | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | ? | - |
? |
pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|
6 | 6.8 | for mono- and diiodinated substrates | Homo sapiens |