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Literature summary for 3.5.1.12 extracted from

  • Hayakawa, K.; Oizumi, J.
    Determination of biotinidase activity by liquid chromatography with fluorometric detection (1986), J. Chromatogr., 383, 148-152.
    View publication on PubMed

Application

Application Comment Organism
medicine plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin Homo sapiens

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
0.05
-
p-(N-biotinylamino)benzoic acid
-
Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
biotin amide + H2O Homo sapiens
-
?
-
?
epsilon-N-biotinyl-L-lysine + H2O Homo sapiens
-
?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
human
-

Purification (Commentary)

Purification (Comment) Organism
-
Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining
blood serum, plasma, leukocytes Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
biotin amide + H2O
-
Homo sapiens ?
-
?
biotinyl-6-aminoquinoline + H2O BAQ, fluorogenic substrate as assay for biotinidase Homo sapiens biotin + 6-aminoquinoline
-
?
epsilon-N-biotinyl-L-lysine + H2O
-
Homo sapiens biotin + L-lysine
-
ir
epsilon-N-biotinyl-L-lysine + H2O
-
Homo sapiens ?
-
?
p-(N-biotinylamino)benzoic acid + H2O
-
Homo sapiens biotin + p-aminobenzoic acid
-
ir