Application | Comment | Organism |
---|---|---|
medicine | plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.05 | - |
p-(N-biotinylamino)benzoic acid | - |
Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | Homo sapiens | - |
? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Homo sapiens | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
human | - |
Purification (Comment) | Organism |
---|---|
- |
Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
blood | serum, plasma, leukocytes | Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | - |
Homo sapiens | ? | - |
? | |
biotinyl-6-aminoquinoline + H2O | BAQ, fluorogenic substrate as assay for biotinidase | Homo sapiens | biotin + 6-aminoquinoline | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | ? | - |
? | |
p-(N-biotinylamino)benzoic acid + H2O | - |
Homo sapiens | biotin + p-aminobenzoic acid | - |
ir |