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Literature summary for 3.4.22.54 extracted from

  • Kramerova, I.; Kudryashova, E.; Tidball, J.G.; Spencer, M.J.
    Null mutation of calpain 3 (p94) in mice causes abnormal sarcomere formation in vivo and in vitro (2004), Hum. Mol. Genet., 13, 1373-1388.
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
titin + H2O Mus musculus calpain 3 expression is required for normal myofibril formation. Calpain 3 may influence the role of titin in sarcomere formation through proteolytic cleavage. The limb girdle muscular dystrophy 2A mutations in calpain C3 influence binding of calpain C3 to titin ?
-
?

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
muscle
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
titin + H2O
-
Mus musculus ?
-
?
titin + H2O calpain 3 expression is required for normal myofibril formation. Calpain 3 may influence the role of titin in sarcomere formation through proteolytic cleavage. The limb girdle muscular dystrophy 2A mutations in calpain C3 influence binding of calpain C3 to titin Mus musculus ?
-
?