Literature summary for 3.4.21.92 extracted from

Hansen, J.; Corydon, T.J.; Palmfeldt, J.; Duerr, A.; Fontaine, B.; Nielsen, M.N.; Christensen, J.H.; Gregersen, N.; Bross, P.
Decreased expression of the mitochondrial matrix proteases Lon and ClpP in cells from a patient with hereditary spastic paraplegia (SPG13) (2008), Neuroscience, 153, 474-482.

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Cloned(Commentary)

Cloned (Comment)	Organism
-	Homo sapiens

Localization

Localization	Comment	Organism	GeneOntology No.	Textmining
mitochondrion	-	Homo sapiens	5739	-

Organism

Organism	UniProt	Comment	Textmining
Homo sapiens	Q16740	-	-

Purification (Commentary)

Purification (Comment)	Organism
-	Homo sapiens

Source Tissue

Source Tissue	Comment	Organism	Textmining
lymphoblastoid cell line	reduced level of the Lon and ClpP proteins in SPG13 patient cells as compared with controls	Homo sapiens	-
additional information	decreased expression of the mitochondrial protein quality control proteases Lon and ClpP, both at the RNA and protein level, in patients with an autosomal dominant form of hereditary spastic paraplegia (SPG13)	Homo sapiens	-
skin fibroblast cell line	reduced level of the Lon and ClpP proteins in SPG13 patient cells as compared with controls	Homo sapiens	-

Synonyms

Synonyms	Comment	Organism
ClpP	-	Homo sapiens

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Release 2023.1 (January 2023)